CASE REPORT: MANAGEMENT OF HIGH-RISK PREGNANCY COMPLICATED BY PLATELET STORAGE POOL DISORDER
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Keywords
Platelet storage pool disorder, multidisciplinary, Post partum hemorrhage.
Abstract
This report presents a case of a 25-year-old primiparous woman booked at our Obstetrics and Gynae OPD on 8th week of gestation. Patient was diagnosed with platelet storage pool disorder on history of prolonged bleeding after cut or injury and menorrhagia. The platelet storage pool disorder is a rare condition but if not managed during antenatal period, it may result in fatal outcome for mother and neonate. The patient had a history of spinal surgery for her disc prolapse. Also, she was obese with body mass index 46, so was categorized as high-risk patient. In this case study we describe how patient was managed through an elective and subsequently emergency cesarean section, by the multidisciplinary team planning. It involved obstetric, hematology, and anesthetic teams to find the risk of postpartum hemorrhage and address the patient's complex needs. The surgical procedure was successfully completed with minimal complications, and both mother and neonate had no uneventful outcome. Patient was discharged with tranexamic acid to be taken orally along with subsequent laboratory investigations for follow up. This case highlights how effective is multidisciplinary approach in managing patients with platelet storage pool disorder.
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